Description

MCT Duocal is a powdered supplement consisting of a blend of carbohydrate and fat, high in medium chain triglycerides (MCT). A food for special medical purposes.

Indications and Prescribability

MCT Duocal can be used as a supplement in the dietary management of conditions requiring extra calories from a combined fat and carbohydrate source, where there is fat malabsorption or where assimilation of LCT’s is impaired.

Suggested Intake

The quantity of MCT Duocal is dependent on the age, bodyweight and medical condition of the patient.  MCT Duocal should be introduced gradually into the diet over a period of days according to the patient’s tolerance.

Preparation & Administration

MCT Duocal can be used to fortify a wide variety of drinks and foods. A range of recipes are available upon request.  MCT Duocal is also useful as an energy enhancer in tube and sip feeds.  MCT Duocal can be mixed with water to form a bland tasting, high energy, low electrolyte liquid. To make a solution of MCT Duocal paste the powder with a small amount of the water prescribed and then add the remaining water, stirring briskly with a fork.

Precautions

Use under medical supervision.
Not suitable for use as a sole source of nutrition.
Not for parenteral use.

Precautions

Store in a cool, dry place.
Always replace the container lid after use.
Once opened use within one month.

Pack Size

MCT Duocal is available in 400g cans.

Description

A powdered (white) carbohydrate energy supplement derived from the hydrolysis of corn starch to produce a glucose polymer of approximately five glucose units.

Indications and Prescribability

Super Soluble Maxijul may be used as an energy enhancer in infant formula, tube feeds and sip feeds.  Super Soluble Maxijul can also be used as a food fortifier to enhance energy intake in a wide range of conditions requiring a high energy, low fluid diet.

Suggested Intake

The quantity of Super Soluble Maxijul should be determined by a clinician or dietitian and is dependent on the age, bodyweight and medical condition of the patient.

Preparation & Administration

Super Soluble Maxijul can easily be incorporated into a wide variety of drinks and foods. Super Soluble Maxijul is also useful as an energy enhancer in tube and sip feeds. Recipe ideas are available upon request.  To make a solution of Super Soluble Maxijul put the required amount of powder into water and stir briskly with a fork, leave to stand until clear.

Precautions

Use under medical supervision.
Use with caution in diabetes.
Not suitable for use as a sole source of nutrition.
Not for parenteral use.

Precautions

Store in a cool dry place.
Always replace the container lid after use.
Once opened, use within one month.

Pack Size

4 x 132g sachets, 200g cans, 2.5kg and 25kg.

Description

Super Soluble Duocal is a powder consisting of a balanced blend of fat and carbohydrate. A food for special medical purposes.

Indications and Prescribability

Super Soluble Duocal can be used for the dietary management of a wide range of conditions where a high energy, low fluid, low electrolyte diet is required such as renal disease, liver disease and catabolic states. Suitable for use in infants, children and adults.

Suggested Intake

The quantity of Super Soluble Duocal should be determined by a clinician or dietitian only and is dependent on the age, bodyweight and medical condition of the patient.

Preparation & Administration

Supplementation of Infant Formula
Care should be taken when supplementing standard infant formula that the protein : energy ratio still meets that recommended for adequate growth and nutrition. Introduce Super Soluble Duocal gradually according to infant tolerance.

1. Initially add 1g Super Soluble Duocal per 100ml Infant formula
2. Increase daily by 1g increments as tolerated by the infant.
3. The usual maximum tolerance is 7g Super Soluble Duocal per 100ml formula in infants under 6 months of age, and 10g Super Soluble Duocal per 100ml formula in infants 6-12 months of age. Consideration should be given to protein: energy ratio when supplementing above 3g per 100ml.

Food Fortification
Super Soluble Duocal is a useful energy enhancer and can be easily incorporated into normal foods and drinks.  Super Soluble Duocal can be added to moist foods by sprinkling on the recommended amount and then stirring thoroughly. Alternatively, Super Soluble Duocal can be made into a paste by gradually adding a small volume of water and then mixing the paste into moist foods. Recipes are available upon request.

Modular Feeds
Super Soluble Duocal can be used as the fat and carbohydrate component of modular feeds or as an energy enhancer in tube or sip feeds.  It is recommended to paste Super Soluble Duocal with a small amount of the feed or water, before adding to ensure thorough mixing.

Precautions

Use under medical supervision.
Not suitable for use as a sole source of nutrition.
Not for parenteral use.

Precautions

Store in a cool, dry place.
Always replace container lid after use.
Once opened use within one month.

Pack Size

Super Soluble Duocal is available in 400g cans.

Description

Liquid Maxijul is a convenient liquid carbohydrate energy source. Liquid Maxijul is a 50% solution of Super Soluble Maxijul in water. Available in Unflavoured and Orange flavour. A food for special medical purposes.

Indications and Prescribability

Liquid Maxijul is a liquid carbohydrate source designed as a supplementary source of nutrition for children and adults for use in the dietary management of conditions requiring a high energy, low fluid diet.

Suggested Intake

The quantity of Liquid Maxijul is dependent on the age, bodyweight and medical condition of the patient.  It is recommended that this product is diluted for children under 5 years of age and possibly for children under 12 years of age.

Preparation & Administration

Liquid Maxijul is a useful energy enhancer and is best served chilled. Liquid Maxijul can also be used to fortify a wide variety of drinks and food.  Liquid Maxijul can be consumed directly from the carton or alternatively can be frozen to make ice lollies.

Precautions

Use under medical supervision.
Use with caution in diabetes.
Flavoured Liquid Maxijul is not recommended for infants under 6 months.
Not suitable for use as a sole source of nutrition.
Not for parenteral use.

Precautions

Store in a cool, dry place.
Once opened store in a refrigerator and consume within 24 hours.

Pack Size

Liquid Maxijul is available in 200ml cartons.

Description

Liquid Duocal is an emulsion consisting of a blend of carbohydrate and fat. A food for special medical purposes.

Indications and Prescribability

Liquid Duocal can be recommended as a dietary supplement to provide a concentrated source of energy for the dietary management of conditions requiring extra calories from a combined fat and carbohydrate source.

Suggested Intake

The quantity of Liquid Duocal should be determined by the clinician or dietitian and is dependent on the age, bodyweight and medical condition of the patient.  Liquid Duocal may require dilution for children under 5 years of age.

Preparation & Administration

Shake well before use.
Liquid Duocal may be taken undiluted or diluted with water. 
Liquid Duocal can be used to fortify a wide variety of drinks and foods and is also useful as an energy enhancer in tube and sip feeds.
Liquid Duocal can also be used as a protein free milk substitute in patients requiring protein restriction.

Precautions

Use under medical supervision.
Not suitable for use as a sole source of nutrition.
Not for parenteral use.

Precautions

Store at ambient temperatures (e.g. 18 - 25°C).
Once opened, keep in a refrigerator and use within 14 days.

Pack Size

Liquid Duocal is available in 250ml bottles.

Description

Anamix is a phenylalanine free drink mix containing essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements. Available in Chocolate (contains colours, sugar and sweeteners), Pineapple & Vanilla flavour (contains colours, sugar and sweeteners), Forest Berries (contains colours, sugar and sweeteners) or Unflavoured. A food for special medical purposes.

Indications and Prescribability

Anamix can be used in the dietary management of children aged 1 - 10 years with proven phenylketonuria (PKU). It contains a balanced blend of essential fatty acids (4:1 ratio). Children with PKU often have a diet high in linoleic acid and thus low levels of α-LA and DHA.
Initial trial results indicate that the use of Anamix may help improve their α-LA status

Suggested Intake

The quantity of Anamix should be determined by a clinician or a dietitian only and is dependent on the age, body weight, and medical condition of the patient.

The diet must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the phenylalanine and general nutrient requirements of the patient.

Preparation & Administration

The recommended dilution is 100mls water plus 1 sachet (29g) of Anamix.

Anamix is easy to mix:

1. Pour the required volume of cold water into a glass or cup.

2. Add the prescribed amount of Anamix and stir.

Anamix is now ready for use.

Anamix is best served chilled.

OSMOLALITY

The osmolality of Anamix at the recommended dilution (1 sachet (29g) plus 100mls water) is:

Unflavoured: 1012 mosm/kg.

Pineapple & Vanilla flavour: 1205 mosm/kg.

Forest Berries flavour: 1210 mosm/kg.

Chocolate: 1205 mosm/kg.

Precautions

Use under medical supervision.

Not suitable for use as a sole source of nutrition.

Not suitable for infants.

Not for parenteral use.

Precautions

Store in a cool dry place.

Shelf life is 1 year

Pack Size

Anamix is available in 30 x 29g sachets.

Description

A white powder containing cholesterol and carbohydrate.

•  Gluten free •  Lactose free

Indications and Prescribability

For medical conditions requiring a source of exogenous cholesterol eg. Smith-Lemli Opitz Syndrome.

Suggested Intake

The recommended dosage of Cholesterol Module is dependent on the age, bodyweight and medical condition of the patient.  It should be determined by a doctor or a dietitian and should be based on serum levels of cholesterol and its metabolites.

Preparation & Administration

Dissolve the correct amount to form a paste and add to a drink or meal.  1 scoop contains 5.9g Cholesterol Module

Osmolality 1:10 dilution = 180 mosm/kg (i.e. 10g product plus 100mls water).

Precautions

Must only be used under strict medical supervision.  Not intended for use as the sole source of nutrition.  Not for parenteral use.

• Free From statement indicates that the highlighted food constituent is not added to the product as an ingredient.

Precautions

Unopened shelf-life as per tin.  Once opened use within four weeks.  Prepared feed can be stored in the refrigerator for up to 24 hours

Pack Size

450g Tin

Description

A nutritionally complete off-white powdered formula high in fat, low in carbohydrate, containing a blend of oils, cow’s milk protein, supplemental amino acids, carbohydrate, vitamins, minerals and trace elements.

Indications and Prescribability

Ketocal Infant can be used to administer the classical long-chain triglyceride (LCT) ketogenic diet (3:1) for the dietary management of intractable epilepsy and other disorders where the ketogenic diet is indicated e.g. disorder of carbohydrate metabolism such as pyruvate dehydrogenase deficiency and glucose transporter type-1 deficiency.  Ketocal Infant can provide complete nutritional support or supplementary feeding for infants and young children from birth to 3 years of age.
A food for special medical purposes.

Suggested Intake

The quantity of feed and dilution should be determined by a clinician or dietitian only and is dependent on the age, bodyweight and medical condition of the patient.

Preparation & Administration

The recommended dilution is 10% w/v ie. 10g powder plus 90mls of water to give a final volume of 100mls.

To ensure that this high fat feed is tolerated when first introducing a ketogenic diet, a less concentrated feed or lower feed volume may need to be provided initially.  Care should be taken to ensure adequate free fluids are still provided.

THE HEALTH OF YOUR INFANT DEPENDS ON CAREFULLY FOLLOWING THE DIRECTIONS FOR PREPARATION AND USE.  INCORRECT PREPARATION CAN MAKE YOUR BABY ILL.

For bottle feeding:

1. Wash hands thoroughly and clean preparation area.  Sterilise feeding and preparation equipment.

2. Ketocal Infant must be made up with hot water (45º - 50ºC or 113º - 122ºF) to fully dissolve.  Pour the required amount of hot water into a sterilised feeding bottle.  To achieve the correct temperature, boil fresh water for 5 minutes and cool to approx 50ºC using a sterile thermometer.  Alternatively, mix water that has been freshly boiled for 5 minutes, with cool water (that has been previously boiled for 5 minutes) in a 1:1 ratio to achieve this temperature.

3. Weigh out the required amount of Ketocal Infant.

4. Add the weighed Ketocal Infant to the water.  Replace the cap on the bottle and shake until the powder dissolves.  The prepared formula must be cooled rapidly to the correct temperature before feeding.  Ensure that the formula is the correct temperature by placing a few drops on the wrist.  Formula should feel warm to the wrist.

5. Formula remaining in the bottle after one hour of feeding should be discarded.  Formula must not be re-warmed during feeding.

For tube or sip feeding

1. Wash hands thoroughly and clean preparation area.  Sterilise feeding and preparation equipment.

2. Ketocal Infant must be made up with hot water (45º - 50ºC or 113º - 122ºF) to fully dissolve.  Pour the required amount of hot water into a sterilised container that seals with a screw top lid. To achieve the correct temperature, boil fresh water for 5 minutes and cool to approx 50ºC using a sterile thermometer.  Alternatively, mix water that has been freshly boiled for 5 minutes, with cool water (that has been previously boiled for 5 minutes) in a 1:1 ratio to achieve this temperature.

3. Weigh out the required amount of Ketocal Infant.

4. Add the weighed Ketocal Infant to the water.  Replace the lid on the container and shake vigorously until the powder dissolves.  The prepared formula must be cooled rapidly to the correct temperature before feeding.

5. Chill in a refrigerator if desired.

6. Shake or stir formula before use.

* Shake or stir formula immediately before use.
* Formula should not be warmed for longer than 15 minutes prior to feeding.
* Do not boil formula and do not use a microwave oven to prepare or warm formula.
* For tube feeding “hang time” should not exceed 4 hours.

On standing, some settling of Ketocal Infant may occur which is a normal feature of the product.  This settling should not block an enteral tube however it is recommended that the tube is flushed with lukewarm water (approximately 37ºC or 99ºF) between each feed.

Precautions

Powdered infant formula is not sterile.  Infant formula should be prepared immediately prior to feeding.

Dental Health Warning

1. When bottle feeding, do not allow prolonged or frequent contact with your baby’s or young child’s teeth since this increases the risk of tooth decay.
2. Make sure their teeth are cleaned after the last feed at night.
3. Ask your Health or Dental Professional for advice.

Precautions

Store in a cool, dry place.  Once opened, reseal can, store in a cool dry place and use within one month.

Pack Size

300g Tin

Description

An orange flavoured phenylalanine-free drink containing a balanced mix of the other essential and non-essential amino acids, carbohydrates, fat (including docosahexanoic acid (DHA)), vitamins, minerals and trace elements.

Indications and Prescribability

For the dietary management of children with phenylketonuria aged 1-10years (3-10years in some countries).

Suggested Intake

The recommended intake of PKU Anamix Junior LQ should be determined by a clinician or dietitian only, and is dependent on age, bodyweight, and medical condition of the patient.

Preparation & Administration

The daily intake of PKU Anamix Junior LQ should be distributed throughout the day.

Precautions

- Use under medical supervision
- Not for parenteral use
- Suitable for children over one year of age
- Not suitable for use as a sole source of nutrition
- Any other: Diet must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the phenylalanine and general nutrition requirements of the patient.

Precautions

Unopened:

Store unopened bottles in a cool, dry place, away from sunlight.

Opened:

Product is best served chilled and consumed immediately.  Unused product should be stored in a refrigerator and consumed within 6 hours

Pack Size

Unit of sale: 36 (6x6) x 125ml

Description

A berry flavoured phenylalanine-free drink containing a balanced mix of the other essential and non-essential amino acids, carbohydrates, fat (including docosahexanoic acid (DHA)), vitamins, minerals and trace elements.

Indications and Prescribability

For the dietary management of children with phenylketonuria aged 1-10years (3-10years in some countries).

Suggested Intake

The recommended intake of PKU Anamix Junior LQ should be determined by a clinician or dietitian only, and is dependent on age, bodyweight, and medical condition of the patient.

Preparation & Administration

The daily intake of PKU Anamix Junior LQ should be distributed throughout the day.

Precautions

- Use under medical supervision
- Not for parenteral use
- Suitable for children over one year of age
- Not suitable for use as a sole source of nutrition
- Any other: Diet must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the phenylalanine and general nutrition requirements of the patient.

Precautions

Unopened:

Store unopened bottles in a cool, dry place, away from sunlight.

Opened:

Product is best served chilled and consumed immediately.  Unused product should be stored in a refrigerator and consumed within 6 hours

Pack Size

Unit of sale: 36 (6x6) x 125ml

Description

Low protein pasta in fun animal shapes

Indications and Prescribability

For the dietary management of conditions requiring restrictions of protein including inherited metabolic disorders, renal or liver failure.

Suggested Intake

The recommended dosage of Low Protein Pasta is dependent on the age, bodyweight and medical condition of the patient

Preparation & Administration

For cooking instructions see pack.

Precautions

Must only be used under strict medical supervision

Precautions

This product can be stored unopened for up to two years in cool, dry conditions.

Pack Size

6 X 500g box

Description

A cream coloured powder consisting of a mixture of essential and non essential amino acids, corn syrup solids, vegetable oil, minerals, trace elements and vitamins. Contains no colouring or flavouring. • Milk protein free • Lactose free

Indications and Prescribability

Neocate One+ is a chemically defined diet based on synthetic amino acids, it is therefore suitable for patients that cannot tolerate protein hydrolysates.  Neocate One+ has been formulated to provide complete nutritional support for children with food allergies, sensitivity to intact protein, intractable malabsorption or following intestinal resection.

Suggested Intake

The quantity of feed and the dilution should be determined by a clinician or dietitian only and is dependent on the age, bodyweight and medical condition of the patient.

The recommended dilution is 1 in 4 weight to volume ie. 100g powder (1 sachet) added to 340ml water yielding a final volume of 400ml.  This dilution provides 1cal / ml.

Neocate One+ may be given in a more dilute concentration if indicated, eg. 100g powder (1 sachet) added to 680ml of water to yield a final volume of 750ml.

Osmolality :  610 mosm / kg* at 25g of product made up to 100ml with water.

Estimated renal solute load : 143 mosm / litre*.

Preparation & Administration

Measure 340ml of cold water into a container and add 1 sachet of Neocate One+ to the water.  Cover and shake the product until the powder has dissolved.  Alternatively this product may be blenderized for up to 10 seconds.  Shake or stir the product immediately before use.

Neocate One+ can be served unflavoured or flavoured using SHS flavours.  Best served chilled.

FOLLOW CAREFULLY THE DIRECTIONS FOR PREPARATION AND USE.  REPEATED USE OF IMPROPERLY PREPARED FORMULA COULD CAUSE ILLNESS.

Precautions

Must only be used under strict medical supervision.  Not for parenteral use.  Not suitable for children under one year of age.

• Free From statement indicates that the highlighted food constituent is not added to the product as an ingredient.

Precautions

This product should be stored in a cool, dry place, in a sealed container.  Once reconstituted the feed should be stored in a refrigerator and consumed within 24 hours.

Pack Size

Neocate One+ is available in boxes of 10x100g packets (10 x 3.5 oz)

Description

An orange flavoured phenylalanine (Phe) free powder containing the remaining essential amino acids (large neutral amino acids and lysine), carbohydrate, fat, vitamins, minerals and trace elements. With sugar and sweetener.

Indications and Prescribability

For the dietary management of adults (over 18 years of age) with proven phenylketonuria (PKU) who are no longer following a phenylalanine restricted diet.

Suggested Intake

The quantity of Lanaflex (Orange) is dependent on the age, bodyweight and medical condition of the individual and is to be determined by a clinician or dietitian only. The recommended quantity of Lanaflex is 0.79g per kg bodyweight per day. This quantity should be distributed over the day in 3 or more portions taken along with meals.  Quantity should not exceed 3 sachets per day in total.

Preparation & Administration

It is recommended that Lanaflex is prepared at an approximate 1 to 4 dilution. In a screw top container add 60mls (2fl. oz) of chilled water. Add the contents of one sachet (15.8g) and shake well until dissolved. This will yield a final volume of 70mls (2.3fl. oz).  The product is best served as a chilled drink and consumed immediately.  If taken in a more concentrated form, water or diluted drinks should be taken immediately after Lanaflex.

It is recommended that an individual on Lanaflex should have a moderate protein restriction of 0.8 g/kg bodyweight per day1. The amount of protein equivalent provided by Lanaflex would need to be subtracted from the total protein requirement, to provide the level of natural protein that can be consumed via the diet.

Referenece1 World Health Organisation. Energy and Protein requirements. Report of a Joint FAO/WHO/UNU Meeting. Geneva: World Health Organisation, 1985.

Precautions

Only intended for use by patients with PKU. Diet must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the phenylalanine and general nutrient requirements of the patient. Not for use when planning or during pregnancy. Seek medical advice before using serotonergic medications.

Precautions

This product should be stored in a cool, dry place.
Opened sachets should be stored in an airtight container and used within 24 hours.

Pack Size

15.8g Sachets

Description

A powder free from phenylalanine but containing a balanced mixture of the other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements. Available in Chocolate, Orange and Unflavoured

Indications and Prescribability

For the dietary management of proven phenylketonuria (PKU) in children over the age of nine years and adults. Suitable for use by pregnant women with PKU. Supplemental iron may need to be provided during pregnancy.

Suggested Intake

The recommended dosage of Periflex Advance is dependent on the age, bodyweight and medical condition of the patient.

Preparation & Administration

Periflex Advance is best served as a chilled drink.  Add the prescribed amount of powder to a shaker, add the desired volume of water and shake.

It is recommended that the patient starts at a 1 to 5 dilution (e.g. 100g Periflex Advance plus 500mls water) and builds up to a 1 to 4 dilution (e.g. 100g Periflex Advance plus 400mls water). 

These dilutions are guidelines only.  Periflex Advance may be given in a more concentrated form e.g. a paste or concentrated drink; water or chilled drinks should be offered at the same time. 

Osmolality
     
1:5 dilution 830 mosm / Kg
1:4 dilution 1060 mosm / Kg

Precautions

Must only be used under strict medical supervision.  Not intended for use as the sole source of nutrition. Not for parenteral use.  Not suitable for metabolic disorders other than PKU. Not intended for infants or young children. Diet must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the phenylalanine and general nutritional requirements of the patient.

Precautions

Store in a cool, dry place.  Always replace container lid after use.  Once opened, use within one month.  Once reconstituted, the prepared feed should be stored in a refrigerator and must not be kept longer than 24 hours from the time of preparation.  Stir or shake immediately before use.

Pack Size

454g Tins

Description

A powder free from phenylalanine but containing a balanced mixture of the other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements. Available in Chocolate, Orange and Unflavoured

Indications and Prescribability

For the dietary management of proven phenylketonuria (PKU) in children over the age of one year

Suggested Intake

The recommended dosage of Periflex Junior is dependent on the age, bodyweight and medical condition of the patient.

Preparation & Administration

Periflex Junior is best served as a chilled drink.  Add the prescribed amount of powder to a shaker, add the desired volume of water and shake.

It is recommended that the patient starts at a 1 to 5 dilution (e.g. 100g Periflex Junior plus 500mls water) and builds up to a 1 to 4 dilution (e.g. 100g Periflex Junior plus 400mls water). 

These dilutions are guidelines only.  Periflex Junior may be given in a more concentrated form e.g. a paste or concentrated drink; water or chilled drinks should be offered at the same time. 

Osmolality

1:5 dilution 720 mosm / Kg
1:4 dilution 910 mosm / Kg

Precautions

Must only be used under strict medical supervision.  Not intended for use as the sole source of nutrition. Not for parenteral use.  Not suitable for metabolic disorders other than PKU. Diet must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the phenylalanine and general nutritional requirements of the patient.

Precautions

Store in a cool, dry place.  Always replace container lid after use.  Once opened, use within one month.  Once reconstituted, the prepared feed should be stored in a refrigerator and must not be kept longer than 24 hours from the time of preparation.  Stir or shake immediately before use.

Pack Size

454g Tins

Description

An orange flavored powder free from phenylalanine but containing a balanced mixture of other essential and non-essential amino acids, vitamins, minerals and trace elements, with minimal levels of carbohydrate, sodium, potassium and chloride. • Phenylalanine free • Milk protein free • Gluten free

Indications and Prescribability

Lophlex (Orange) is for the dietary management of proven Phenylketonuria (PKU) in children from approximately 9 years of age and adults.  Suitable for use by pregnant women with PKU provided iron requirements are supplemented from dietary or other sources.

Suggested Intake

The recommended intake of Lophlex will vary depending on the age, bodyweight and medical condition of the individual.  Intake should be adjusted to maintain normal growth and development.  For accuracy, Lophlex should be weighed on a gram scale.  The daily intake of Lophlex should be divided into equal portions and distributed throughout the day.  This product is best consumed with meals.

Preparation & Administration

USE ONLY UNDER THE DIRECTION OF A PHYSICIAN OR DIETITIAN.
Lophlex (Orange) must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet phenylalanine and general nutrition requirements.

Make a paste of the prescribed amount of powder with a small volume of water.  Gradually add sufficient water to yield the required volume. It is recommended that Lophlex be reconstituted at a 1 in 5 dilution (e.g. 100g of Lophlex made up to 500 ml with water or one sachet made up to approximately 70ml with water) and advanced to a 1 in 3 dilution if desired (e.g. 100g Lophlex made up to 300ml with water or one sachet made up to approximately 43ml with water).  These dilutions are guidelines only. Lophlex may be given in a more concentrated form as either a drink or a paste.  Water or diluted drinks should be offered at the same time as Lophlex.  To ensure tolerance, Lophlex may initially need to be introduced at a lower concentration. 

Lophlex is best prepared with chilled water and consumed immediately after preparation

Osmolality

1 in 5 dilution: 1390 mosm/kg

Precautions

Must only be used under strict medical supervision.  Not intended for use as the sole source of nutrition.  Not suitable for infants under one year of age.  Not for parenteral use.  Not suitable for metabolic disorders other than PKU or as a supplement for individuals who do not have PKU. 

This product must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the phenylalanine and general nutritional requirements of the patient.

• Free from statement indicates that the highlighted food constituent is not added to the product as an ingredient.

Precautions

Store in a cool dry place.  Do not store at extreme temperature.

Pack Size

14.3g sachets

Description

An orange flavored powder free from methionine, threonine and valine, and low in isoleucine, but containing balanced amounts of the other essential and non-essential amino acids, carbohydrates, vitamins, minerals and trace elements. • Methionine free • Threonine free • Valine free • Gluten free

Indications and Prescribability

XMTVI Maxamum (Flavored) is for the dietary management of proven Propionic or Methylmalonic Acidemia in children from approximately 9 years of age and adults.

Suggested Intake

The recommended intake of XMTVI Maxamum (Flavored) will vary depending on the age, bodyweight and medical condition of the individual.  Intake should be adjusted to maintain normal growth and development.  For accuracy, XMTVI Maxamum should be weighed on a gram scale.  The daily intake of XMTVI Maxamum should be divided into equal portions and distributed throughout the day.

Preparation & Administration

USE ONLY UNDER THE DIRECTION OF A PHYSICIAN OR DIETITIAN.

XMTVI Maxamum (Flavored) must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet methionine, threonine valine, isoleucine and general nutrition requirements.

XMTVI Maxamum (Flavored) is best served with meals.  Make a paste of the prescribed amount of powder with a small volume of water.  Gradually add sufficient water to yield the prescribed volume.  It is recommended that XMTVI Maxamum be reconstituted at a 1 to 7 dilution (e.g. 100g of XMTVI Maxamum plus 700ml of water) and advanced to a 1 to 5 dilution (e.g. 100g of XMTVI Maxamum and 500ml of water).  These dilutions are guidelines only. XMTVI Maxamum may be given in a more concentrated form e.g. drink or paste.  Water or diluted drinks should be offered at the same time as Maxamum.

XMTVI Maxamum (Flavored) is best prepared with chilled water and consumed immediately after preparation.  Reconstituted drink mix should be stored in the refrigerator and used within 24 hours.

Precautions

Must only be used under strict medical supervision.  Not intended for use as the sole source of nutrition.  Not for parenteral use.  Not intended for infants or young children.  Not suitable for metabolic disorders other than Propionic or Methylmalonic Acidemia.

This product must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the methionine, threonine, valine,  isoleucine and general nutrition requirements of the patient.

• Free from statement indicates that the highlighted food constituent is not added to the product as an ingredient.

Precautions

Store unopened can at room temperature.  Do not store at extreme temperatures.  Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month.

Pack Size

454g Tins

Description

An orange flavored powder free from methionine but containing balanced amounts of the other essential and non-essential amino acids, carbohydrates, vitamins, minerals and trace elements. • Methionine free • Gluten free

Indications and Prescribability

XMet Maxamum (Flavored) is for the dietary management of proven Hypermethioninaemia or Vitamin B6 non-responsive Homocystinuria in children from approximately 9 years of age and adults. Suitable for use by pregnant women with Hypermethioninaemia or Vitamin B6 non-responsive Homocystinuria.  Supplemental iron may need to be provided during pregnancy.

Suggested Intake

The recommended intake of XMet Maxamum (Flavored) will vary depending on the age, bodyweight and medical condition of the individual.  Intake should be adjusted to maintain normal growth and development.  For accuracy, XMet Maxamum should be weighed on a gram scale.  The daily intake of XMet Maxamum should be divided into equal portions and distributed throughout the day.

Preparation & Administration

USE ONLY UNDER THE DIRECTION OF A PHYSICIAN OR DIETITIAN.

XMet Maxamum (Flavored) must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet methionine and general nutrition requirements.

XMet Maxamum (Flavored) is best served with meals.  Make a paste of the prescribed amount of powder with a small volume of water.  Gradually add sufficient water to yield the prescribed volume.  It is recommended that XMet Maxamum be reconstituted at a 1 to 7 dilution (e.g. 100g of XMet Maxamum plus 700ml of water) and advanced to a 1 to 5 dilution (e.g. 100g of XMet Maxamum and 500ml of water).  These dilutions are guidelines only. XMet Maxamum may be given in a more concentrated form e.g. drink or paste.  Water or diluted drinks should be offered at the same time as Maxamum.

XMet Maxamum (Flavored) is best prepared with chilled water and consumed immediately after preparation.  Reconstituted drink mix should be stored in the refrigerator and used within 24 hours.

Precautions

Must only be used under strict medical supervision.  Not intended for use as the sole source of nutrition.  Not for parenteral use.  Not intended for infants or young children.  Not suitable for metabolic disorders other than Hypermethioninaemia or Vitamin B6 non-responsive Homocystinuria.

This product must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the methionine and general nutrition requirements of the patient.

• Free from statement indicates that the highlighted food constituent is not added to the product as an ingredient.

Precautions

Store unopened can at room temperature.  Do not store at extreme temperatures.  Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month.

Pack Size

454g Tins

Description

An orange flavored powder free from leucine but containing balanced amounts of the other essential and non-essential amino acids, carbohydrates, vitamins, minerals and trace elements. • Leucine free • Gluten free

Indications and Prescribability

XLeu Maxamum (Flavored) is for the dietary management of proven Isovaleric Acidemia in children from approximately 9 years of age and adults.

Suggested Intake

The recommended intake of XLeu Maxamum (Flavored) will vary depending on the age, bodyweight and medical condition of the individual.  Intake should be adjusted to maintain normal growth and development.  For accuracy, XLeu Maxamum should be weighed on a gram scale.  The daily intake of XLeu Maxamum should be divided into equal portions and distributed throughout the day

Preparation & Administration

USE ONLY UNDER THE DIRECTION OF A PHYSICIAN OR DIETITIAN.

XLeu Maxamum (Flavored) must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet leucine and general nutrition requirements.

XLeu Maxamum (Flavored) is best served with meals.  Make a paste of the prescribed amount of powder with a small volume of water.  Gradually add sufficient water to yield the prescribed volume.  It is recommended that XLeu Maxamum be reconstituted at a 1 to 7 dilution (e.g. 100g of XLeu Maxamum plus 700ml of water) and advanced to a 1 to 5 dilution (e.g. 100g of XLeu Maxamum and 500ml of water).  These dilutions are guidelines only. XLeu Maxamum may be given in a more concentrated form e.g. drink or paste.  Water or diluted drinks should be offered at the same time as Maxamum.

XLeu Maxamum (Flavored) is best prepared with chilled water and consumed immediately after preparation.  Reconstituted drink mix should be stored in the refrigerator and used within 24 hours.

Precautions

Must only be used under strict medical supervision.  Not intended for use as the sole source of nutrition.  Not for parenteral use.  Not intended for infants or young children.  Not suitable for metabolic disorders other than Isovaleric Acidemia.

This product must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the leucine and general nutrition requirements of the patient.

• Free from statement indicates that the highlighted food constituent is not added to the product as an ingredient.

Precautions

Store unopened can at room temperature.  Do not store at extreme temperatures.  Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month.

Pack Size

454g Tins

Description

An orange flavored powder free from leucine, isoleucine and valine but containing balanced amounts of the other essential and non-essential amino acids, carbohydrates, vitamins, minerals and trace elements. • Leucine free • Isoleucine free • Valine free • Gluten free

Indications and Prescribability

MSUD Maxamum (Flavored) is for the dietary management of proven Maple Syrup Urine Disease (MSUD) in children from approximately 9 years of age and adults.

Suggested Intake

The recommended intake of MSUD Maxamum (Flavored) will vary depending on the age, bodyweight and medical condition of the individual.  Intake should be adjusted to maintain normal growth and development.  For accuracy, MSUD Maxamum should be weighed on a gram scale.  The daily intake of MSUD Maxamum should be divided into equal portions and distributed throughout the day.

Preparation & Administration

USE ONLY UNDER THE DIRECTION OF A PHYSICIAN OR DIETITIAN.

MSUD Maxamum (Flavored) must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet leucine, isoleucine, valine and general nutrition requirements.

MSUD Maxamum (Flavored) is best served with meals.  Make a paste of the prescribed amount of powder with a small volume of water.  Gradually add sufficient water to yield the prescribed volume.  It is recommended that MSUD Maxamum be reconstituted at a 1 to 7 dilution (e.g. 100g of MSUD Maxamum plus 700ml of water) and advanced to a 1 to 5 dilution (e.g. 100g of MSUD Maxamum and 500ml of water).  These dilutions are guidelines only. MSUD Maxamum may be given in a more concentrated form e.g. drink or paste.  Water or diluted drinks should be offered at the same time as Maxamum.

MSUD Maxamum (Flavored) is best prepared with chilled water and consumed immediately after preparation.  Reconstituted drink mix should be stored in the refrigerator and used within 24 hours.

Precautions

Must only be used under strict medical supervision.  Not intended for use as the sole source of nutrition.  Not for parenteral use.  Not intended for infants or young children.  Not suitable for metabolic disorders other than MSUD.

This product must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the leucine, isoleucine, valine and general nutrition requirements of the patient.

• Free from statement indicates that the highlighted food constituent is not added to the product as an ingredient.

Precautions

Store unopened can at room temperature.  Do not store at extreme temperatures.  Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month.

Pack Size

454g Tins

Description

An unflavored powder free from phenylalanine but containing balanced amounts of the other essential and non-essential amino acids, carbohydrates, vitamins, minerals and trace elements. Also available in Orange and Forest Berries flavours

Indications and Prescribability

XPhe Maxamum (Unflavored) is for the dietary management of proven phenylketonuria (PKU) in children from approximately 9 years of age and adults.  Suitable for use by pregnant women with PKU.  Supplemental iron may need to be provided during pregnancy.

Suggested Intake

The recommended intake of XPhe Maxamum will vary depending on the age, bodyweight and medical condition of the individual.  Intake should be adjusted to maintain normal growth and development.  For accuracy, XPhe Maxamum should be weighed on a gram scale.  The daily intake of XPhe Maxamum should be divided into equal portions and distributed throughout the day. 

Preparation & Administration

USE ONLY UNDER THE DIRECTION OF A PHYSICIAN OR DIETITIAN.

XPhe Maxamum must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet phenylalanine and general nutrition requirements.

XPhe Maxamum is best served with meals.  Make a paste of the prescribed amount of powder with a small volume of water.  Gradually add sufficient water to yield the prescribed volume.  It is recommended that XPhe Maxamum be reconstituted at a 1 to 7 dilution (e.g. 100g of XPhe Maxamum plus 700 mL of water or one sachet plus 350ml water) and advanced to a 1 to 5 dilution (e.g. 100g of XPhe Maxamum plus 500 mL of water or one sachet plus 250ml water).  These dilutions are guidelines only. XPhe Maxamum may be given in a more concentrated form i.e. drink or paste.  Water or diluted drinks should be offered at the same time as Maxamum.

XPhe Maxamum is best prepared with chilled water and consumed immediately after preparation.  Reconstituted drink mix should be stored in the refrigerator and used within 24 hours.

Precautions

Must only be used under strict medical supervision.  Not intended for use as the sole source of nutrition.  Not for parenteral use.  Not intended for infants or young children.  Not suitable for metabolic disorders other than phenylketonuria.

This product must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the phenylalanine and general nutrition requirements of the patient

Precautions

Store unopened can at room temperature.  Do not store at extreme temperatures.  Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month

Pack Size

454g tins.
30 x 50g sachets.

Description

An orange flavored powder free from phenylalanine and tyrosine but containing a balanced mixture of the other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements.

Indications and Prescribability

XPhe, XTyr Maxamaid is for use in the dietary management of proven Tyrosinaemia in children from approximately 1 to 8 years of age where plasma methionine levels are normal.

Suggested Intake

The recommended intake or XPhe XTyr Maxamaid will vary depending on the age, bodyweight and medical condition of the individual.  Intake should be adjusted to maintain normal growth and development.  For accuracy, XPhe XTyr Maxamaid should be weighed on a gram scale.  The daily intake of XPhe XTyr Maxamaid should be divided into equal portions and distributed throughout the day. 

Preparation & Administration

USE ONLY UNDER THE DIRECTION OF A PHYSICIAN OR DIETITIAN.
XPhe XTyr Maxamaid must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet phenylalanine, tyrosine and general nutrition requirements.

XPhe XTyr Maxamaid is best served with meals.  Make a paste of the prescribed amount of powder with a small volume of water.  Gradually add sufficient water to yield the prescribed volume.  It is recommended that XPhe XTyr Maxamaid be reconstituted at a 1 to 7 dilution (e.g. 100g of XPhe XTyr Maxamaid plus 700 mL of water) and advanced to a 1 to 5 dilution (e.g. 100g of XPhe XTyr Maxamaid plus 500 mL of water).  These dilutions are guidelines only. XPhe XTyr Maxamaid may be given in a more concentrated form i.e. drink or paste.  Water or diluted drinks should be offered at the same time as XPhe XTyr Maxamaid.

XPhe XTyr Maxamaid is best prepared with chilled water and consumed immediately after preparation.  Reconstituted drink mix should be stored in the refrigerator and used within 24 hours.

HOUSEHOLD MEASUREMENTS
1 cup = 145g powder….................½ cup = 70g powder
¼ cup = 35g powder…..................1 Tbsp = 9g powder

Above weights are approximate only.  For accuracy use a gram scale.

Osmolality
A 1:7 dilution = 680 mOsm/kg
A 1:5 dilution = 940 mOsm/kg

Precautions

Must only be used under strict medical supervision.  Not intended for use as the sole source of nutrition.  Not recommended for infants under 1 year of age.  Not for parenteral use.  Not suitable for metabolic disorders other than Tyrosinaemia or as a supplement for individuals who do not have Tyrosinaemia. 

This product must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the phenylalanine, tyrosine and general nutrition requirements of the patient.

Precautions

Store unopened can at room temperature.  Do not store at extreme temperatures.  Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month.

Pack Size

454g Tins

Description

An orange flavoured powder free from methionine, threonine and valine and low in isoleucine but containing a balanced mixture of the other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements.

Indications and Prescribability

XMTVI Maxamaid is for use in the dietary management of proven Propionic or Methylmalonic Acidaemia in children from approximately 1 to 8 years of age.

Suggested Intake

The recommended intake or XMTVI Maxamaid will vary depending on the age, bodyweight and medical condition of the individual.  Intake should be adjusted to maintain normal growth and development.  For accuracy, XMTVI Maxamaid should be weighed on a gram scale.  The daily intake of XMTVI Maxamaid should be divided into equal portions and distributed throughout the day.

Preparation & Administration

USE ONLY UNDER THE DIRECTION OF A PHYSICIAN OR DIETITIAN.

XMTVI Maxamaid must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet methionine, threonine, valine, isoleucine and general nutrition requirements.

XMTVI Maxamaid is best served with meals.  Make a paste of the prescribed amount of powder with a small volume of water.  Gradually add sufficient water to yield the prescribed volume.  It is recommended that XMTVI Maxamaid be reconstituted at a 1 to 7 dilution (e.g. 100g of XMTVI Maxamaid plus 700 mL of water) and advanced to a 1 to 5 dilution (e.g. 100g of XMTVI Maxamaid plus 500 mL of water).  These dilutions are guidelines only. XMTVI Maxamaid may be given in a more concentrated form i.e. drink or paste.  Water or diluted drinks should be offered at the same time as XMTVI Maxamaid.

XMTVI Maxamaid is best prepared with chilled water and consumed immediately after preparation.  Reconstituted drink mix should be stored in the refrigerator and used within 24 hours.

HOUSEHOLD MEASUREMENTS
1 cup = 145g powder….................½ cup = 70g powder
¼ cup = 35g powder….................1 Tbsp = 9g powder

Above weights are approximate only.  For accuracy use a gram scale.
 
Osmolality
A 1:7 dilution = 680 mOsm/kg
A 1:5 dilution = 940 mOsm/kg

Precautions

Must only be used under strict medical supervision.  Not intended for use as the sole source of nutrition.  Not recommended for infants under 1 year of age.  Not for parenteral use.  Not suitable for metabolic disorders other than Propionic or Methylmalonic Acidaemia or as a supplement for individuals who do not have Propionic or Methylmalonic Acidaemia. 

This product must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the methionine, threonine, valine, isoleucine and general nutrition requirements of the patient.

Precautions

Store unopened can at room temperature.  Do not store at extreme temperatures.  Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month.

Pack Size

454g Tins

Description

An orange flavored powder free from methionine but containing a balanced mixture of the other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements.

Indications and Prescribability

XMet Maxamaid is for use in the dietary management of Hypermethionemia and vitamin B6 Non-Responsive Homocystinuria children from approximately 1 to 8 years of age

Suggested Intake

The recommended intake or XMet Maxamaid will vary depending on the age, bodyweight and medical condition of the individual.  Intake should be adjusted to maintain normal growth and development.  For accuracy, XMet Maxamaid should be weighed on a gram scale.  The daily intake of XMet Maxamaid should be divided into equal portions and distributed throughout the day. 

Preparation & Administration

USE ONLY UNDER THE DIRECTION OF A PHYSICIAN OR DIETITIAN.

XMet Maxamaid must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet methionine and general nutrition requirements.
XMet Maxamaid is best served with meals.  Make a paste of the prescribed amount of powder with a small volume of water.  Gradually add sufficient water to yield the prescribed volume.  It is recommended that XMet Maxamaid be reconstituted at a 1 to 7 dilution (e.g. 100g of XMet Maxamaid plus 700 mL of water) and advanced to a 1 to 5 dilution (e.g. 100g of XMet Maxamaid plus 500 mL of water).  These dilutions are guidelines only. XMet Maxamaid may be given in a more concentrated form i.e. drink or paste.  Water or diluted drinks should be offered at the same time as XMet Maxamaid.

XMet Maxamaid is best prepared with chilled water and consumed immediately after preparation.  Reconstituted drink mix should be stored in the refrigerator and used within 24 hours.

HOUSEHOLD MEASUREMENTS (to be completed after first new batch available)
1 cup = 145g powder….................½ cup = 70g powder
¼ cup = 35g powder…..................1 Tbsp = 9g powder

Above weights are approximate only.  For accuracy use a gram scale.
 

Osmolality
A 1:7 dilution = 680 mOsm/kg
A 1:5 dilution = 940 mOsm/kg

Precautions

Must only be used under strict medical supervision. Not intended for use as the sole source of nutrition.  Not recommended for infants under 1 year of age.  Not for parenteral use.  Not suitable for metabolic disorders other than Hypermethionemia and vitamin B6 Non-Responsive Homocystinuria or as a supplement for individuals who do not have Hypermethionemia and vitamin B6 Non-Homocystinuria. 

This product must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the methionine and general nutrition requirements of the patient.

Precautions

Store unopened can at room temperature.  Do not store at extreme temperatures.  Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month.

Pack Size

454g Tins

Description

An orange flavored powder free from leucine but containing a balanced mixture of the other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements. * Leucine Free

Indications and Prescribability

XLeu Maxamaid is for use in the dietary management of Isovaleric Acidaemia in children from approximately 1 to 8 years of age.

Suggested Intake

XLeu Maxamaid intake will vary depending on the age, bodyweight and medical condition of the child.  Intake is adjusted to maintain normal growth and development.  100g of XLeu Maxamaid provides 25g of protein equivalent.  For accuracy, XLeu Maxamaid should be weighed on a gram scale.

Preparation & Administration

USE ONLY UNDER THE DIRECTION OF A PHYSICIAN OR DIETITIAN.

XLeu Maxamaid must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet leucine and general nutrition requirements.

XLeu Maxamaid is best served as a chilled drink with meals.  Make a paste of the prescribed amount of powder with a small volume of water.  Gradually add sufficient water to yield the prescribed volume.  It is recommended that XLeu Maxamaid be reconstituted at a 1 to 7 dilution (e.g. 100g of XLeu Maxamaid and 700ml of water) and advanced to a 1 to 5 dilution (e.g. 100g of XLeu Maxamaid and 500ml of water).  These dilutions are guidelines only.  XLeu Maxamaid may be given in a more concentrated form i.e. drink or paste; water or diluted drinks should be offered at the same time.

Reconstituted drink mix should be stored in the refrigerator and used within 24 hours.

HOUSEHOLD MEASUREMENTS
1 cup = 145g powder….................½ cup = 70g powder
¼ cup = 35g powder…..................1 Tbsp = 9g powder

Above weights are approximate only.  For accuracy use a gram scale.

Osmolality    
A 1:7 dilution = 680 mOsm/kg
A 1:5 dilution = 940 mOsm/kg

Precautions

Must only be used under strict medical supervision.  Not intended for use as the sole source of nutrition.  Not recommended for infants under 1 year of age.  Not for parenteral use.  Not suitable for metabolic disorders other than Isovaleric Acidaemia or as a supplement for individuals who do not have Isovaleric Acidaemia. 

This product must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the leucine and general nutrition requirements of the patient.

• Free from statement indicates that the highlighted food constituent is not added to the product as an ingredient.

Precautions

Store unopened can at room temperature.  Do not store at extreme temperatures.  Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month.

Pack Size

454g Tins

Description

An orange flavored powder free from leucine, isoleucine and valine but containing a balanced mixture of the other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements. *Leucine Free *Isoleucine Free *Valine Free

Indications and Prescribability

MSUD Maxamaid (Flavored) is for use in the dietary management of proven maple syrup urine disease (MSUD) in children from approximately 1 to 8 years of age.

Suggested Intake

MSUD Maxamaid intake will vary depending on the age, bodyweight and medical condition of the child.  Intake is adjusted to maintain normal growth and development.  100g of MSUD Maxamaid provides 25g of protein equivalent.  For accuracy, MSUD Maxamaid should be weighed on a gram scale

Preparation & Administration

USE ONLY UNDER THE DIRECTION OF A PHYSICIAN OR DIETITIAN.

MSUD Maxamaid must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet isoleucine, leucine, valine and general nutrition requirements.

MSUD Maxamaid is best served as a chilled drink with meals.  Make a paste of the prescribed amount of powder with a small volume of water.  Gradually add sufficient water to yield the prescribed volume.  It is recommended that MSUD Maxamaid be reconstituted at a 1 to 7 dilution (e.g. 100g of MSUD Maxamaid and 700ml of water) and advanced to a 1 to 5 dilution (e.g. 100g of MSUD Maxamaid and 500ml of water).  These dilutions are guidelines only.  MSUD Maxamaid may be given in a more concentrated form i.e. drink or paste; water or diluted drinks should be offered at the same time.

Reconstituted drink mix should be stored in the refrigerator and used within 24 hours.

HOUSEHOLD MEASUREMENTS
1 cup = 145g powder…......................½ cup = 70g powder
¼ cup = 35g powder….......................1 Tbsp = 9g powder
Above weights are approximate only.  For accuracy use a gram scale.

Osmolality    
A 1:7 dilution = 680 mOsm/kg
A 1:5 dilution = 940 mOsm/kg

Precautions

Must only be used under strict medical supervision.  Not intended for use as the sole source of nutrition.  Not recommended for infants under 1 year of age.  Not for parenteral use.  Not suitable for metabolic disorders other than MSUD or as a supplement for individuals who do not have MSUD. 

This product must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the leucine, isoleucine, valine, and general nutrition requirements of the patient.

• Free From statement indicates that the highlighted food constituent is not added to the product as an ingredient.

Precautions

Store unopened can at room temperature.  Do not store at extreme temperatures.  Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month.

Pack Size

454g tins

Description

XPTM Analog is for use in the dietary management of proven tryrosinaemia type I in infants from birth to one year • Phenylalanine free • Tyrosine free • Methionine free • Gluten free • Lactose free • Fructose free

Indications and Prescribability

XPTM Analog is for use in the dietary management of proven tryrosinaemia type I in infants from birth to one year.  The product may also be used for young children, older than one year, depending on their weight, age and clinical condition

Suggested Intake

The recommended dosage of XPTM Analog is dependent on the age, bodyweight and medical condition of the patient

Preparation & Administration

THE HEALTH OF YOUR INFANT DEPENDS ON CAREFULLY FOLLOWING THE DIRECTIONS FOR PREPARATION AND USE.  USE ONLY AS DIRECTED BY PHYSICIAN.  DILUTE PROPERLY.  REPEATED USE OF IMPROPERLY PREPARED FORMULA COULD CAUSE ILLNESS.

XPTM Analog should not be used as the sole source of protein but must be given in conjunction with a protein source eg. breast milk or proprietary infant formulain quantities prescribed by a dietitian or physician to supply the phenylalanine, tyrosine, methionine and general nutritional requirements of the patient, and to ensure normal growth.

The recommended dosage of XPTM Analog is dependent on the age, bodyweight and medical condition of the patient.  Each unpacked, level scoop (5g) of XPTM Analog requires 1 fl.oz (30ml) of water to yield a recommended concentration of 15% w/v (21 cal/fl.oz).  For accuracy, XPTM Analog should be weighed on a gram scale.

Mixing Instructions:
1. Wash hands.  Sterilize bottle feeding system.
2. Boil water for 5 minutes.  Cool boiled water to a warm temperature.
3. Add the prescribed amount of XPTM Analog powder and a protein source to the sterilized feeding bottle.
4. Pour the required amount of warm water into feeding bottle.  To make the recommended dilution (21 kcal/fl.oz), XPTM Analog requires 1 fl.oz (30ml) of water for every 5g (1 scoop) of powder.  Place cap on bottle and shake until the powder has dissolved.
5. Before feeding, make sure that the formula is lukewarm by placing a few drops on the wrist.  Store prepared formula in the refrigerator and use within 24 hrs of preparation.  Shake immediately before use.
CAUTION: Do not boil formula.  Do not use a microwave oven to prepare or warm formula.  Discard unused formula remaining in the bottle after feeding.

HOUSEHOLD MEASUREMENTS:
1 cup   =  115g powder ½ cup   =  55g powder
¼ cup =  30g powder                       1 Tbsp   = 8g powder

Above weights are approximations only.  For accuracy use a gram scale.

Osmolality     377 mosm / kg.
(15% w/v ie. 15g XPTM Analog made up to 100mls with water).

Estimated Renal Solute Load   173 mosm / litre.

Precautions

Must only be used under strict medical supervision.  Not for parenteral use.  XPTM Analog should not be used as the sole source of protein but must be given in conjunction with a protein source eg. breast milk or proprietary infant formulain quantities prescribed by a dietitian or physician to supply the phenylalanine, tyrosine, methionine and general nutritional requirements of the patient, and to ensure normal growth.

* Free From statement indicates that the highlighted food constituent is not added to the product as an ingredient.

Precautions

Store in a cool, dry place.  Once opened, use within one month.  Always replace container lid after use.  Once reconstituted, feed should be stored in a refrigerator and must not be kept longer than 24 hours from time of preparation.  Stir or shake immediately before use

Pack Size

400g Can

Description

XPhe XTyr Analog is for use in the dietary management of proven tyrosinaemia when plasma methionine is normal, in infants from birth to one year • Phenylalanine free • Tyrosine free • Gluten free • Lactose free • Fructose free

Indications and Prescribability

XPhe XTyr Analog is for use in the dietary management of proven tyrosinaemia when plasma methionine is normal, in infants from birth to one year.  The product may be used for young children older than one year, depending on their weight, age and clinical condition.

Suggested Intake

The recommended dosage of XPhe XTyr Analog is dependent on the age, bodyweight and medical condition of the patient

Preparation & Administration

THE HEALTH OF YOUR INFANT DEPENDS ON CAREFULLY FOLLOWING THE DIRECTIONS FOR PREPARATION AND USE.  USE ONLY AS DIRECTED BY PHYSICIAN.  DILUTE PROPERLY.  REPEATED USE OF IMPROPERLY PREPARED FORMULA COULD CAUSE ILLNESS.

XPhe XTyr Analog should not be used as the sole source of protein but must be given in conjunction with a protein source eg. breast milk or proprietary infant formula in quantities prescribed by a dietitian or physician to supply the phenylalanine, tyrosine and general nutritional requirements of the patient, and to ensure normal growth.

The recommended dosage of XPhe XTyr Analog is dependent on the age, bodyweight and medical condition of the patient.  Each unpacked, level scoop (5g) of XPhe XTyr Analog requires 1 fl.oz (30ml) of water to yield a recommended concentration of 15% w/v (21 cal/fl.oz).  For accuracy, XPhe XTyr Analog should be weighed on a gram scale.

Mixing Instructions:
1. Wash hands.  Sterilize bottle feeding system.
2. Boil water for 5 minutes.  Cool boiled water to a warm temperature.
3. Add the prescribed amount of XPhe XTyr Analog powder and a protein source to the sterilized feeding bottle.
4. Pour the required amount of warm water into feeding bottle.  To make the recommended dilution (21 kcal/fl.oz), XPhe XTyr Analog requires 1 fl.oz (30ml) of water for every 5g (1 scoop) of powder.  Place cap on bottle and shake until the powder has dissolved.
5. Before feeding, make sure that the formula is lukewarm by placing a few drops on the wrist.  Store prepared formula in the refrigerator and use within 24 hrs of preparation.  Shake immediately before use.

CAUTION: Do not boil formula.  Do not use a microwave oven to prepare or warm formula.  Discard unused formula remaining in the bottle after feeding.

HOUSEHOLD MEASUREMENTS:
1 cup   =  115g powder ½ cup   =  55g powder
¼ cup =  30g powder                       1 Tbsp   = 8g powder

Above weights are approximations only.  For accuracy use a gram scale.

Osmolality      377 mosm / kg.
(15% w/v ie. 15g XPhe XTyr Analog, made up to 100mls with water)

Estimated Renal Solute Load   173 mosm / litre.

Precautions

Must only be used under strict medical supervision.  Not for parenteral use.  XPhe XTyr Analog should not be used as the sole source of protein but must be given in conjunction with a protein source eg. breast milk or proprietary infant formula in quantities prescribed by a dietitian or physician to supply the phenylalanine, tyrosine and general nutritional requirements of the patient, and to ensure normal growth.

* Free From statement indicates that the highlighted food constituent is not added to the product as an ingredient.

Precautions

Store in a cool, dry place.  Once opened, use within one month.  Always replace container lid after use.  Once reconstituted, feed should be stored in a refrigerator and must not be kept longer than 24 hours from time of preparation.  Stir or shake immediately before use.

Pack Size

400g Can

Description

XMTVI Analog is for use in the dietary management of proven methylmalonic or proprionic acidaemia in infants from birth to one year • Methionine free • Threonine free • Valine free • Gluten free • Lactose free • Fructose free

Indications and Prescribability

XMTVI Analog is for use in the dietary management of proven methylmalonic or proprionic acidaemia in infants from birth to one year

Suggested Intake

The recommended dosage of XMTVI Analog is dependent on the age, bodyweight and medical condition of the patient

Preparation & Administration

THE HEALTH OF YOUR INFANT DEPENDS ON CAREFULLY FOLLOWING THE DIRECTIONS FOR PREPARATION AND USE.  USE ONLY AS DIRECTED BY PHYSICIAN.  DILUTE PROPERLY.  REPEATED USE OF IMPROPERLY PREPARED FORMULA COULD CAUSE ILLNESS.

XMTVI Analog should not be used as the sole source of protein but must be given in conjunction with a protein source eg. breast milk or proprietary infant formula in quantities prescribed by a dietitian or physcician to supply the methionine, threonine, valine, isoleucine and general nutritional requirements of the patient, and to ensure normal growth.

The recommended dosage of XMTVI Analog is dependent on the age, bodyweight and medical condition of the patient.  Each unpacked, level scoop (5g) of XMTVI Analog requires 1 fl.oz (30ml) of water to yield a recommended concentration of 15% w/v (21 cal/fl.oz).  For accuracy, XMTVI Analog should be weighed on a gram scale.

Mixing Instructions:
1. Wash hands.  Sterilize bottle feeding system.
2. Boil water for 5 minutes.  Cool boiled water to a warm temperature.
3. Add the prescribed amount of XMTVI Analog powder and a protein source to the sterilized feeding bottle.
4. Pour the required amount of warm water into feeding bottle.  To make the recommended dilution (21 kcal/fl.oz), XMTVI Analog requires 1 fl.oz (30ml) of water for every 5g (1 scoop) of powder.  Place cap on bottle and shake until the powder has dissolved.
5. Before feeding, make sure that the formula is lukewarm by placing a few drops on the wrist.  Store prepared formula in the refrigerator and use within 24 hrs of preparation.  Shake immediately before use.

CAUTION: Do not boil formula.  Do not use a microwave oven to prepare or warm formula.  Discard unused formula remaining in the bottle after feeding.

HOUSEHOLD MEASUREMENTS:
1 cup   =  115g powder ½ cup   =  55g powder
¼ cup =  30g powder                       1 Tbsp   = 8g powder

Above weights are approximations only.  For accuracy use a gram scale.

Osmolality      377 mosm / kg.
(15% w/v ie. 15g XMTVI Analog, made up to 100mls with water).

Estimated Renal Solute Load   173 mosm / litre.

Precautions

Must only be used under strict medical supervision.  Not for parenteral use.  XMTVI Analog should not be used as the sole source of protein but must be given in conjunction with a protein source eg. breast milk or proprietary infant formula in quantities prescribed by a dietitian or physcician to supply the methionine, threonine, valine, isoleucine and general nutritional requirements of the patient, and to ensure normal growth.

* Free From statement indicates that the highlighted food constituent is not added to the product as an ingredient.

Precautions

Store in a cool, dry place.  Once opened, use within one month.  Always replace container lid after use.  Once reconstituted, feed should be stored in a refrigerator and must not be kept longer than 24 hours from time of preparation.  Stir or shake immediately before use.

Pack Size

400g Can

Description

XMet Analog is for the dietary management of proven Vitamin B6 non-responsive homocystinuria or hypermethioninaemia in infants from birth to one year • Methionine free • Gluten free • Lactose free • Fructose free

Indications and Prescribability

XMet Analog is for the dietary management of proven Vitamin B6 non-responsive homocystinuria or hypermethioninaemia in infants from birth to one year.  The product may also be used for young children, older than one year depending on their weight, age and clinical condition

Suggested Intake

The recommended dosage of XMet Analog is dependent on the age, bodyweight and medical condition of the patient

Preparation & Administration

THE HEALTH OF YOUR INFANT DEPENDS ON CAREFULLY FOLLOWING THE DIRECTIONS FOR PREPARATION AND USE.  USE ONLY AS DIRECTED BY PHYSICIAN.  DILUTE PROPERLY.  REPEATED USE OF IMPROPERLY PREPARED FORMULA COULD CAUSE ILLNESS.

XMet Analog should not be used as the sole source of protein but must be given in conjunction with a protein source eg. breast milk or proprietary infant formula in quantities prescribed by a dietitian or physician, to supply the methionine and general nutritional requirements of the patient and to ensure normal growth.

The recommended dosage of XMet Analog is dependent on the age, bodyweight and medical condition of the patient.  Each unpacked, level scoop (5g) of XMet Analog requires 1 fl.oz (30ml) of water to yield a recommended concentration of 15% w/v (21 cal/fl.oz).  For accuracy, XMet Analog should be weighed on a gram scale.

Mixing Instructions:

1. Wash hands.  Sterilize bottle feeding system.
2. Boil water for 5 minutes.  Cool boiled water to a warm temperature.
3. Add the prescribed amount of XMet Analog powder and a protein source to the sterilized feeding bottle.
4. Pour the required amount of warm water into feeding bottle.  To make the recommended dilution (21 kcal/fl.oz), XMet Analog requires 1 fl.oz (30ml) of water for every 5g (1 scoop) of powder.  Place cap on bottle and shake until the powder has dissolved.
5. Before feeding, make sure that the formula is lukewarm by placing a few drops on the wrist.  Store prepared formula in the refrigerator and use within 24 hrs of preparation.  Shake immediately before use.

CAUTION: Do not boil formula.  Do not use a microwave oven to prepare or warm formula.  Discard unused formula remaining in the bottle after feeding.

HOUSEHOLD MEASUREMENTS:
1 cup   =  115g powder ½ cup   =  55g powder
¼ cup =  30g powder                       1 Tbsp   = 8g powder

Above weights are approximations only.  For accuracy use a gram scale.

Osmolality      377 mosm / kg.
(15% w/v ie. 15g XMET Analog made up to 100mls with water)

Estimated Renal Solute Load    173 mosm / litre.

Precautions

Must only be used under strict medical supervision.  Not for parenteral use.  XMet Analog should not be used as the sole source of protein but must be given in conjunction with a protein source eg. breast milk or proprietary infant formula in quantities prescribed by a dietitian or physician, to supply the methionine and general nutritional requirements of the patient and to ensure normal growth.

* Free From statement indicates that the highlighted food constituent is not added to the product as an ingredient.

Precautions

Store in a cool, dry place.  Once opened, use within one month.  Always replace container lid after use.  Once reconstituted, feed should be stored in a refrigerator and must not be kept longer than 24 hours from time of preparation.  Stir or shake immediately before use.

Pack Size

400g Can

Description

XLys, XTrp Analog is for use in the dietary management of proven Glutaric Acidemia type I in infants from birth to one year • Lysine free • Tryptophan free • Gluten free • Lactose free

Indications and Prescribability

XLys, XTrp Analog is for use in the dietary management of proven Glutaric Acidemia type I in infants from birth to one year.  The product may also be used for children older than one year depending on the weight, age and clinical condition.

Suggested Intake

The recommended dosage of XLys XTrp Analog is dependent on the age, bodyweight and medical condition of the patient

Preparation & Administration

THE HEALTH OF YOUR INFANT DEPENDS ON CAREFULLY FOLLOWING THE DIRECTIONS FOR PREPARATION AND USE.  USE ONLY AS DIRECTED BY PHYSICIAN.  DILUTE PROPERLY.  REPEATED USE OF IMPROPERLY PREPARED FORMULA COULD CAUSE ILLNESS.

XLys XTrp Analog should not be used as the sole source of protein but must be given in conjunction with a protein source eg. breast milk or proprietary infant formula in quantities prescribed by a dietitian or physician to supply the lysine, tryptophan and general nutritional requirements of the patient and to ensure normal growth.

The recommended dosage of XLys XTrp Analog is dependent on the age, bodyweight and medical condition of the patient.  Each unpacked, level scoop (5g) of XLys XTrp Analog requires 1 fl.oz (30ml) of water to yield a recommended concentration of 15% w/v (21 cal/fl.oz).  For accuracy, XLys XTrp Analog should be weighed on a gram scale.

Mixing Instructions:
1. Wash hands.  Sterilize bottle feeding system.
2. Boil water for 5 minutes.  Cool boiled water to a warm temperature.
3. Add the prescribed amount of XLys XTrp Analog powder and a protein source to the sterilized feeding bottle.
4. Pour the required amount of warm water into feeding bottle.  To make the recommended dilution (21 kcal/fl.oz), XLys XTrp Analog requires 1 fl.oz (30ml) of water for every 5g (1 scoop) of powder.  Place cap on bottle and shake until the powder has dissolved.
5. Before feeding, make sure that the formula is lukewarm by placing a few drops on the wrist.  Store prepared formula in the refrigerator and use within 24 hrs of preparation.  Shake immediately before use.

CAUTION: Do not boil formula.  Do not use a microwave oven to prepare or warm formula.  Discard unused formula remaining in the bottle after feeding.

HOUSEHOLD MEASUREMENTS:
1 cup   =  115g powder ½ cup   =  55g powder
¼ cup =  30g powder                       1 Tbsp   = 8g powder

Above weights are approximations only.  For accuracy use a gram scale.

Osmolality  377 mosm / kg.
(15% w/v ie. 15g XLys XTrp Analog made up to 100mls with water).

Estimated Renal Solute Load  173 mosm / litre.

Precautions

Must only be used under strict medical supervision.  Not for parenteral use.  XLys XTrp Analog should not be used as the sole source of protein but must be given in conjunction with a protein source eg. breast milk or proprietary infant formula in quantities prescribed by a dietitian or physician to supply the lysine, tryptophan and general nutritional requirements of the patient and to ensure normal growth.

* Free From statement indicates that the highlighted food constituent is not added to the product as an ingredient.

Precautions

Store in a cool, dry place.  Once opened, use within one month.  Always replace container lid after use.  Once reconstituted, feed should be stored in a refrigerator and must not be kept longer than 24 hours from time of preparation.  Stir or shake immediately before use.

Pack Size

400g Can

Description

XLeu Analog is for use in the dietary management of proven isovaleric acidaemia, or other proven disorders of leucine metabolism in infants from birth to one year • Leucine free • Gluten free • Lactose free • Fructose free * Free From statement indicates that the highlighted food constituent is not added to the product as an ingredient.

Indications and Prescribability

XLeu Analog is for use in the dietary management of proven isovaleric acidaemia, or other proven disorders of leucine metabolism in infants from birth to one year.  The product may be used for young children, older than one year depending on their weight, age and clinical condition.

Suggested Intake

The recommended dosage of XLeu Analog is dependent on the age, bodyweight and medical condition of the patient.

Preparation & Administration

THE HEALTH OF YOUR INFANT DEPENDS ON CAREFULLY FOLLOWING THE DIRECTIONS FOR PREPARATION AND USE.  USE ONLY AS DIRECTED BY PHYSICIAN.  DILUTE PROPERLY.  REPEATED USE OF IMPROPERLY PREPARED FORMULA COULD CAUSE ILLNESS.

Xleu Analog should not be used as the sole source of protein but must be given in conjunction with a protein source eg. breast milk or proprietary infant formula in quantities prescribed by a dietitian or physician to supply the leucine and general nutritional requirements of the patient, and to ensure normal growth.

The recommended dosage of XLeu Analog is dependent on the age, bodyweight and medical condition of the patient.  Each unpacked, level scoop (5g) of XLeu Analog requires 1 fl.oz (30ml) of water to yield a recommended concentration of 15% w/v (21 cal/fl.oz).  For accuracy, XLeu Analog should be weighed on a gram scale.

Mixing Instructions:
1. Wash hands.  Sterilize bottle feeding system.
2. Boil water for 5 minutes.  Cool boiled water to a warm temperature.
3. Add the prescribed amount of XLeu Analog powder and a protein source to the sterilized feeding bottle.
4. Pour the required amount of warm water into feeding bottle.  To make the recommended dilution (21 kcal/fl.oz), XLeu Analog requires 1 fl.oz (30ml) of water for every 5g (1 scoop) of powder.  Place cap on bottle and shake until the powder has dissolved.
5. Before feeding, make sure that the formula is lukewarm by placing a few drops on the wrist.  Store prepared formula in the refrigerator and use within 24 hrs of preparation.  Shake immediately before use.

CAUTION: Do not boil formula.  Do not use a microwave oven to prepare or warm formula.  Discard unused formula remaining in the bottle after feeding.

Precautions

Must only be used under strict medical supervision.  Not for parenteral use.  XLeu Analog should not be used as the sole source of protein but must be given in conjunction with a protein source eg. breast milk or proprietary infant formula in quantities prescribed by a dietitian or physician to supply the leucine and general nutritional requirements of the patient, and to ensure normal growth.

Precautions

Store in a cool, dry place.  Once opened, use within one month.  Always replace container lid after use.  Once reconstituted, feed should be stored in a refrigerator and must not be kept longer than 24 hours from time of preparation.  Stir or shake immediately before use.

Pack Size

400g Can

Description

MSUD Analog is for use in the dietary management of proven Maple Syrup Urine Disease in infants from birth to one year. The product may also be used for young children older than one year depending on their weight, age and clinical condition. • Isoleucine free • Leucine free • Valine free • Gluten free • Lactose free • Fructose free * Free From statement indicates that the highlighted food constituent is not added to the product as an ingredient.

Indications and Prescribability

MSUD Analog is for use in the dietary management of proven Maple Syrup Urine Disease in infants from birth to one year.  The product may also be used for young children older than one year depending on their weight, age and clinical condition.

Suggested Intake

The recommended dosage of MSUD Analog is dependent on the age, bodyweight and medical condition of the patient

Preparation & Administration

THE HEALTH OF YOUR INFANT DEPENDS ON CAREFULLY FOLLOWING THE DIRECTIONS FOR PREPARATION AND USE.  USE ONLY AS DIRECTED BY PHYSICIAN.  DILUTE PROPERLY.  REPEATED USE OF IMPROPERLY PREPARED FORMULA COULD CAUSE ILLNESS.

MSUD Analog should not be used as the sole source of protein, but must be given in conjunction with a protein source eg. breast milk or proprietary infant formula in quantities prescribed by a dietitian or physician to supply the isoleucine, leucine, valine and general nutritional requirements of the patient, and to ensure normal growth.

The recommended dosage of MSUD Analog is dependent on the age, bodyweight and medical condition of the patient.  Each unpacked, level scoop (5g) of MSUD Analog requires 1 fl.oz (30ml) of water to yield a recommended concentration of 15% w/v (21 cal/fl.oz).  For accuracy, MSUD Analog should be weighed on a gram scale.

Mixing Instructions:
1. Wash hands.  Sterilize bottle feeding system.
2. Boil water for 5 minutes.  Cool boiled water to a warm temperature.
3. Add the prescribed amount of MSUD Analog powder and a protein source to the sterilized feeding bottle.
4. Pour the required amount of warm water into feeding bottle.  To make the recommended dilution (21 kcal/fl.oz), MSUD Analog requires 1 fl.oz (30ml) of water for every 5g (1 scoop) of powder.  Place cap on bottle and shake until the powder has dissolved.
5. Before feeding, make sure that the formula is lukewarm by placing a few drops on the wrist.  Store prepared formula in the refrigerator and use within 24 hrs of preparation.  Shake immediately before use.

CAUTION: Do not boil formula.  Do not use a microwave oven to prepare or warm formula.  Discard unused formula remaining in the bottle after feeding.

HOUSEHOLD MEASUREMENTS:
1 cup   =  115g powder ½ cup   =  55g powder
¼ cup =  30g powder                       1 Tbsp   = 8g powder

Above weights are approximations only.  For accuracy use a gram scale.

Precautions

Must only be used under strict medical supervision.  Not for parenteral use.  MSUD Analog should not be used as the sole source of protein, but must be given in conjunction with a protein source eg. breast milk or proprietary infant formula in quantities prescribed by a dietitian or physician to supply the isoleucine, leucine, valine and general nutritional requirements of the patient, and to ensure normal growth.

Precautions

Store in a cool, dry place.  Once opened, use within one month.  Always replace container lid after use.  Once reconstituted, feed should be stored in a refrigerator and must not be kept longer than 24 hours from time of preparation.  Stir or shake immediately before use.

Pack Size

400g Can

Description

A pineapple flavoured, leucine, isoleucine and valine-free powdered medical food for use in the dietary management of proven Maple Syrup Urine Disease (MSUD) in children over the age of one year

Indications and Prescribability

For use in the dietary management of proven Maple Syrup Urine Disease (MSUD) in children over the age of one year.

Suggested Intake

The recommended dosage of Acerflex is dependent on the age, bodyweight and medical condition of the patient.

Preparation & Administration

Acerflex is best served as a chilled drink with meals.  Make a paste of the prescribed amount of powder with a small quantity of water.  Gradually add sufficient water to yield the prescribed volume. 

It is recommended that Acerflex be reconstituted at a 1 to 5 dilution (e.g. 100g Acerflex and 500ml of water) and advance to 1 to 4 dilution (e.g. 100g Acerflex and 400ml of water). 

These dilutions are guidelines only.  Acerflex may be given in a more concentrated form e.g. drink or paste; water or diluted drinks should be offered at the same time.

Osmolality

1 to 5 dilution – 670 mosm / kg
1 to 4 dilution – 830 mosm / kg

Precautions

Must only be used under strict medical supervision.  Not intended for use as the sole source of nutrition.  Diet must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the leucine, isoleucine, valine and general nutritional requirements of the patient.  Not for parenteral use.

• Free From statement indicates that the highlighted food constituent is not added to the product as an ingredient.

Precautions

Store in a cool, dry place.  Always replace container lid after use.  Once opened, use within one month. Once reconstituted, the prepared feed should be stored in a refrigerator and must not be kept longer than 24 hours from the time of preparation.  Stir or shake immediately before use.

Pack Size

4 x 454g cans

Description

A hypoallergenic, nutritionally complete, powdered medical food consisting of a mixture of essential and non-essential amino acids, corn syrup solids, vegetable oil, minerals, trace elements and vitamins. Artificially flavored with chocolate flavor

Indications and Prescribability

Neocate Junior Chocolate Flavor is an elemental medical food based on free amino acids; therefore it is suitable for those patients who cannot tolerate protein hydrolysates.  Neocate Junior Chocolate Flavor has been formulated to provide complete or supplemental nutritional support for children over one year of age with gastrointestinal impairment due to milk protein insensitivity or other medical conditions affecting the gastrointestinal tract requiring an elemental diet

Suggested Intake

The recommended quantity of Neocate Junior Chocolate Flavor is dependent on the age, bodyweight and medical condition of the patient.  The recommended dilution is 30 Cal/fl.oz.

Preparation & Administration

This can be achieved by mixing the following amounts of powder and water.  Each scoop weighs 8.2g.

Add Powder….......Add Water….......Final Volume

2 scoops or 16.4g…..2 fl.oz (60ml).....2.5 fl.oz. (75ml)

4 scoops or 32.8g…..4 fl.oz (120ml).....5 fl.oz (150ml)

7 scoops or 57.4g….7 fl.oz (200ml).....8 fl.oz. (240ml)

20 scoops or 164g…..20 fl.oz (600ml).....24 fl.oz (720ml)

2 cups + 1 tbsp or 223g…..28 fl.oz (840ml).....33.5 fl.oz. (1000ml)

Household Measurements:
1 cup = 108g 1 tbsp = 7g
½ cup = 54g 1 tsp = 2.1g
¼ cup = 27g
1/3 cup = 36g

The above weights and volumes are approximations only. For accuracy, use a gram scale.

Precautions

DO NOT USE BOILING WATER TO PREPARE THE FEED.  DO NOT BOIL PREPARED FEED.

Precautions

This product should be stored in a cool dry place. Once opened, use within one month

Pack Size

400g Cans

Description

A flavoured phenylalanine-free liquid containing a balanced mixture of the other essential and non-essential amino acids, vitamins, trace elements and some minerals. A food for special medical purposes

Indications and Prescribability

For use in the dietary management of proven Phenylketonuria (PKU) in children aged 4+ years and adults including pregnant women with proven Phenylketonuria.

Suggested Intake

The recommended dosage of Lophlex LQ 10 is dependent on the age, bodyweight and medical condition of the patient and should be determined by a clinician or dietitian only

Preparation & Administration

The daily intake of Lophlex LQ 10 should be distributed throughout the day.  Water or diluted drinks should be offered / taken at the same time as Lophlex LQ. 

Lophlex LQ 10 is best served chilled. Shake vigorously before use.

Part consumed pouches can be stored in a fridge for up to 24 hours. Shake vigorously before use.

Precautions

Must only be used under strict medical supervision.  Not intended for use as the sole source of nutrition.  Not for parenteral use.  Not suitable for metabolic disorders other than PKU or as a supplement for individuals who do not have PKU.

This product must be supplemented with natural protein, fluid and other nutrients in medically prescribed quantities to supply the phenylalanine and general nutritional requirements of the patient.  Lophlex LQ contains only trace amounts of sodium, potassium and chloride.

Precautions

Store at room temperature away from sunlight.

Pack Size

(3 x 125ml) x 10
60 x 62.5 ml

Description

Pizza Bases for Low Protein Diet

Indications and Prescribability

For use in the dietary management of inherited metabolic disorders, renal or liver disease requiring a low protein diet.

*  Milk protein free *  Gluten free *  Lactose free *  Egg free
*  Soya free

* Free From statement indicates that the highlighted food constituent is not added to the product as an ingredient

Suggested Intake

Preparation & Administration

Cooking Instructions

1. Preheat oven to 200oC/400oF/Gas Mark 6
2. Remove all packaging
3. Top the pizza to your taste and bake in the oven for 10-12 minutes

NB: Times given are for guidance only, as variations between different appliances can occur.

Precautions

Must only be used under strict medical supervision.  Not suitable for sodium restricted diets.

Precautions

The Pizza Bases have a shelf-life of 12 weeks from date of manufacture.  Store in a cool dry place.

Pack Size

2 x 180g

Description

Low protein cinnamon flavoured cookies

Indications and Prescribability

Available on prescription for the dietary management of phenylketonuria, other inborn errors of metabolism, renal failure, liver cirrhosis, coeliac disease and other gluten sensitive enteropathies such as dermatitis herpetiformis.

Suggested Intake

Preparation & Administration

Precautions

Only to be used under medical supervision.  Not intended for use as the sole source of nutrition. Not for parenteral use.

Not for use in soya-free diets.

Precautions

Store in a cool, dry place. Consume prior to the best before date shown on the packaging. The shelf life of Juvela Low Protein Cinnamon Flavour Cookies is 18 months

Pack Size

Available in 150g packs. Each pack contains approximately 30 cookies

Description

Low protein orange flavour cookies

Indications and Prescribability

Available on prescription for the dietary management of phenylketonuria, other inborn errors of metabolism, renal failure, liver cirrhosis, coeliac disease and other gluten sensitive enteropathies such as dermatitis herpetiformis.

This product is free from gluten, milk, lactose and egg.

Suggested Intake

Preparation & Administration

Precautions

Only to be used under strict medical supervision.  Not intended for use as the sole source of nutrition. Not for parenteral use.

Not for use soya-free diets.

Precautions

Store in a cool, dry place. Consume prior to best before date shown on packaging. Juvela Low Protein Orange Flavour Cookies have a shelf life of 18 months.

Pack Size

Available in 150g packs. Each pack contains approximately 26 cookies

Description

Low protein chocolate chip cookie

Indications and Prescribability

Available on prescription for the dietary management of phenylketonuria, other inborn errors of metabolism, renal failure, liver cirrhosis, coeliac disease and other gluten sensitive enteropathies such as dermatitis herpetiformis.

This product is free from gluten, milk, lactose, and egg.

Suggested Intake

Preparation & Administration

Precautions

Only to be used under medical supervision. Not intended for use as the sole source of nutrition. Not for parenteral use.

Not for use in soya-free diets

Precautions

Store in a cool, dry place. Consume prior to the best before date shown on the packaging. The shelf life of Juvela Low Protein Chocolate Chip Cookies is 18 months

Pack Size

Available in 130g packs. Each pack contains approximately 26 cookies

Description

Low protein white bread rolls

Indications and Prescribability

Available on prescription for the dietary management of phenylketonuria, other inborn errors of metabolism, renal failure, liver cirrhosis, celiac disease and other gluten sensitive enteropathies such as dermatitis herpetiformis

Suggested Intake

Preparation & Administration

Precautions

Only to be used under medical supervision.  Not intended for use as the sole source of nutrition.  Not for parenteral use.

Precautions

Store in a cool, dry place.  Consume before best before date stated on the packaging. 

The shelf life of Juvela Low Protein Rolls is 13 weeks

Pack Size

Available in 3 x 5 x 400g packs

Description

Low protein all purpose mix. A sachet of yeast is provided in each pack

Indications and Prescribability

Available on prescription for the dietary management of phenylketonuria, other inborn errors of metabolism, renal failure, liver cirrhosis, coeliac disease and other gluten sensitive enteropathies such as dermatitis herpetiformis.

This product is free from gluten, milk, egg, lactose and soya.

Suggested Intake

Preparation & Administration

Precautions

Only to be used under medical supervision.  Not intended for use as the sole source of nutrition. Not for parental use.
Not for use in wheat-free diets.

Precautions

Store in a cool, dry place. Use prior to best before date shown on packaging. The shelf life of Juvela Low Protein Mix is 14 months

Pack Size

Available in 500g packs with 8.5g of dried yeast (sachet)

Description

A nutritionally complete amino acid-based powdered infant formula, with long chain polyunsaturated fatty acids (LC PUFA’s), docosahexaenoic acid (DHA) and arachidonic acid (ARA). • Hypoallergenic • Milk Protein Free

Indications and Prescribability

For the dietary management of infants with Cow Milk Allergy, Multiple Food Protein Intolerance and other conditions where an elemental diet is recommended.

A food for special medical purposes.

Suggested Intake

The quantity of feed and the dilution should be determined by a clinician or dietitian only and is dependent on the age, bodyweight and medical condition of the infant

Preparation & Administration

THE HEALTH OF YOUR INFANT DEPENDS ON CAREFULLY FOLLOWING THE DIRECTIONS FOR PREPARATION AND USE.  INCORRECT PREPARATION CAN MAKE YOUR BABY ILL.
Each level scoop (4.9g) of Neocate LCP requires 30ml (approx. 1 fl. oz) of water to yield the recommended feed concentration (14.7%).

1. Wash hands thoroughly and clean preparation area.  Sterilise bottles and teats.

2. Boil fresh water for 5 minutes and allow to cool for at least 30 minutes so that it feels warm to the wrist.  Pour the required amount of water into a sterilised feeding bottle.

3. Fill the scoop provided with Neocate LCP and level off with a clean, dry knife.  Do not press the powder into the scoop.  Only use the scoop provided.

4. Add the prescribed number of scoops of Neocate LCP to the water.  Replace the cap on the bottle and shake until the powder dissolves.  Before feeding, ensure that the formula is at the correct temperature by placing a few drops on the wrist.

5. Formula remaining in the bottle after one hour of feeding should be discarded.  Formula must not be re-warmed during feeding.

Precautions

Important Notice:  Powdered infant formula is not sterile.  Infant formula should be prepared immediately prior to feeding

Precautions

Store in a cool, dry place.  Once can is opened, use within one month.

Pack Size

Neocate LCP is available in 400g cans.

Description

Add-ins is a flavourless phenylalanine-free powder containing balanced amounts of the other essential and non-essential amino acids, fat, vitamins, trace elements, calcium, phosphorus and magnesium.

Indications and Prescribability

For the dietary management of proven phenylketonuria (PKU) in individuals over 4 years of age. A Food for Special Medical Purposes (Medical Food).

Use under medical supervision. Suitable for individuals over 4 years of age. Not suitable as a sole source of nutrition. Not for parenteral use.  Not suitable for metabolic disorders other than PKU, or as a supplement for individuals who do not have PKU.

Suggested Intake

The recommended intake of Add Ins is dependent on the age, bodyweight and medical condition of the patient

Preparation & Administration

For best results, stir Add-Ins powder gently into warm/cold foods (less than 60ºC) and serve immediately. Add Ins should be used as part of the daily protein substitute requirements. Hot foods may need to be cooled prior to the addition of Add-Ins

Precautions

Only intended for use by patients with proven PKU. Diet must be supplemented with natural protein and other nutrients in medically prescribed quantities to supply the phenylalanine and general nutritional requirements of the patient. Add Ins only contains trace amounts of sodium, potassium or chloride.

Precautions

Store in a cool, dry place

Pack Size

60 x 18.2g (0.64oz) sachets

Description

Low protein egg replacer for use in baking

Indications and Prescribability

For use in the dietary management inherited metabolic disorders, renal or liver failure requiring a low protein diet. A food for special medical purposes.

Suggested Intake

This low protein food is classed as a ‘free food’ in the UK, other countries may have different guidelines.  Please check with your healthcare professional or dietitian.

Preparation & Administration

The recommended dosage of Low Protein Egg Replacer is dependant on the age, bodyweight and medical condition of the patient.

Precautions

Must only be used under strict medical supervision. Not suitable as a sole source of nutrition.

Precautions

This product should be stored in cool dry conditions, out of direct sunlight. Once opened, a sachet should be stored in an airtight container and used within 3 months.

Pack Size

6 x 500g

Description

Low Protein Pasta

Indications and Prescribability

For use in the dietary management inherited metabolic disorders, renal or liver failure requiring a low protein diet. A food for special medical purposes.

Suggested Intake

This low protein food is classified as a ‘free food’ in the UK, other countries may have different guidelines.  Please check with your Healthcare Professional or Dietitian.

Preparation & Administration

For cooking instructions, see pack.

Precautions

Must only be used under strict medical supervision. Not suitable as a sole source of nutrition.

Precautions

This product should be stored in a cool dry place.

Pack Size

6 x 500g

Description

Low Protein Pasta

Indications and Prescribability

For use in the dietary management inherited metabolic disorders, renal or liver failure requiring a low protein diet. A food for special medical purposes.

Suggested Intake

This low protein food is classified as a ‘free food’ in the UK, other countries may have different guidelines.  Please check with your Healthcare Professional or Dietitian.

Preparation & Administration

The recommended dosage of Low Protein Pasta is dependant on the age, bodyweight and medical condition of the patient. For cooking instructions, see pack.

Precautions

Must only be used under strict medical supervision. Not suitable as a sole source of nutrition.

Precautions

This product should be stored in a cool dry place.

Pack Size

12x250g